Dergi makalesi Açık Erişim
Trautmann, Agnes; Bodria, Monica; Ozaltin, Fatih; Gheisari, Alaleh; Melk, Anette; Azocar, Marta; Anarat, Ali; Caliskan, Salim; Emma, Francesco; Gellermann, Jutta; Oh, Jun; Baskin, Esra; Ksiazek, Joanna; Remuzzi, Giuseppe; Erdogan, Ozlem; Akman, Sema; Dusek, Jiri; Davitaia, Tinatin; Oezkaya, Ozan; Papachristou, Fotios; Papachristou, Fotios
<?xml version='1.0' encoding='utf-8'?> <resource xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance" xmlns="http://datacite.org/schema/kernel-4" xsi:schemaLocation="http://datacite.org/schema/kernel-4 http://schema.datacite.org/meta/kernel-4.1/metadata.xsd"> <identifier identifierType="URL">https://aperta.ulakbim.gov.tr/record/82601</identifier> <creators> <creator> <creatorName>Trautmann, Agnes</creatorName> <givenName>Agnes</givenName> <familyName>Trautmann</familyName> </creator> <creator> <creatorName>Bodria, Monica</creatorName> <givenName>Monica</givenName> <familyName>Bodria</familyName> </creator> <creator> <creatorName>Ozaltin, Fatih</creatorName> <givenName>Fatih</givenName> <familyName>Ozaltin</familyName> </creator> <creator> <creatorName>Gheisari, Alaleh</creatorName> <givenName>Alaleh</givenName> <familyName>Gheisari</familyName> </creator> <creator> <creatorName>Melk, Anette</creatorName> <givenName>Anette</givenName> <familyName>Melk</familyName> </creator> <creator> <creatorName>Azocar, Marta</creatorName> <givenName>Marta</givenName> <familyName>Azocar</familyName> </creator> <creator> <creatorName>Anarat, Ali</creatorName> <givenName>Ali</givenName> <familyName>Anarat</familyName> </creator> <creator> <creatorName>Caliskan, Salim</creatorName> <givenName>Salim</givenName> <familyName>Caliskan</familyName> </creator> <creator> <creatorName>Emma, Francesco</creatorName> <givenName>Francesco</givenName> <familyName>Emma</familyName> </creator> <creator> <creatorName>Gellermann, Jutta</creatorName> <givenName>Jutta</givenName> <familyName>Gellermann</familyName> </creator> <creator> <creatorName>Oh, Jun</creatorName> <givenName>Jun</givenName> <familyName>Oh</familyName> </creator> <creator> <creatorName>Baskin, Esra</creatorName> <givenName>Esra</givenName> <familyName>Baskin</familyName> </creator> <creator> <creatorName>Ksiazek, Joanna</creatorName> <givenName>Joanna</givenName> <familyName>Ksiazek</familyName> </creator> <creator> <creatorName>Remuzzi, Giuseppe</creatorName> <givenName>Giuseppe</givenName> <familyName>Remuzzi</familyName> </creator> <creator> <creatorName>Erdogan, Ozlem</creatorName> <givenName>Ozlem</givenName> <familyName>Erdogan</familyName> </creator> <creator> <creatorName>Akman, Sema</creatorName> <givenName>Sema</givenName> <familyName>Akman</familyName> </creator> <creator> <creatorName>Dusek, Jiri</creatorName> <givenName>Jiri</givenName> <familyName>Dusek</familyName> </creator> <creator> <creatorName>Davitaia, Tinatin</creatorName> <givenName>Tinatin</givenName> <familyName>Davitaia</familyName> </creator> <creator> <creatorName>Oezkaya, Ozan</creatorName> <givenName>Ozan</givenName> <familyName>Oezkaya</familyName> </creator> <creator> <creatorName>Papachristou, Fotios</creatorName> <givenName>Fotios</givenName> <familyName>Papachristou</familyName> </creator> <creator> <creatorName>Papachristou, Fotios</creatorName> <givenName>Fotios</givenName> <familyName>Papachristou</familyName> </creator> </creators> <titles> <title>Spectrum Of Steroid-Resistant And Congenital Nephrotic Syndrome In Children: The Podonet Registry Cohort</title> </titles> <publisher>Aperta</publisher> <publicationYear>2015</publicationYear> <dates> <date dateType="Issued">2015-01-01</date> </dates> <resourceType resourceTypeGeneral="Text">Journal article</resourceType> <alternateIdentifiers> <alternateIdentifier alternateIdentifierType="url">https://aperta.ulakbim.gov.tr/record/82601</alternateIdentifier> </alternateIdentifiers> <relatedIdentifiers> <relatedIdentifier relatedIdentifierType="DOI" relationType="IsIdenticalTo">10.2215/CJN.06260614</relatedIdentifier> </relatedIdentifiers> <rightsList> <rights rightsURI="http://www.opendefinition.org/licenses/cc-by">Creative Commons Attribution</rights> <rights rightsURI="info:eu-repo/semantics/openAccess">Open Access</rights> </rightsList> <descriptions> <description descriptionType="Abstract">Background and objectives Steroid-resistant nephrotic syndrome is a rare kidney disease involving either immune-mediated or genetic alterations of podocyte structure and function. The rare nature, heterogeneity, and slow evolution of the disorder are major obstacles to systematic genotype-phenotype, intervention, and outcome studies, hampering the development of evidence-based diagnostic and therapeutic concepts. To overcome these limitations, the PodoNet Consortium has created an international registry for congenital nephrotic syndrome and childhood-onset steroid-resistant nephrotic syndrome.</description> </descriptions> </resource>
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