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Exploring the Clinical and Genetic Spectrum of Steroid Resistant Nephrotic Syndrome: The PodoNet Registry

Trautmann, Agnes; Lipska-Zietkiewicz, Beata S.; Schaefer, Franz


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  <identifier identifierType="URL">https://aperta.ulakbim.gov.tr/record/29971</identifier>
  <creators>
    <creator>
      <creatorName>Trautmann, Agnes</creatorName>
      <givenName>Agnes</givenName>
      <familyName>Trautmann</familyName>
      <affiliation>Univ Ctr Pediat &amp; Adolescent Med, Div Pediat Nephrol, Heidelberg, Germany</affiliation>
    </creator>
    <creator>
      <creatorName>Lipska-Zietkiewicz, Beata S.</creatorName>
      <givenName>Beata S.</givenName>
      <familyName>Lipska-Zietkiewicz</familyName>
      <affiliation>Med Univ Gdansk, Dept Biol &amp; Med Genet, Clin Genet Unit, Gdansk, Poland</affiliation>
    </creator>
    <creator>
      <creatorName>Schaefer, Franz</creatorName>
      <givenName>Franz</givenName>
      <familyName>Schaefer</familyName>
      <affiliation>Univ Ctr Pediat &amp; Adolescent Med, Div Pediat Nephrol, Heidelberg, Germany</affiliation>
    </creator>
  </creators>
  <titles>
    <title>Exploring The Clinical And Genetic Spectrum Of Steroid Resistant Nephrotic Syndrome: The Podonet Registry</title>
  </titles>
  <publisher>Aperta</publisher>
  <publicationYear>2018</publicationYear>
  <dates>
    <date dateType="Issued">2018-01-01</date>
  </dates>
  <resourceType resourceTypeGeneral="Text">Journal article</resourceType>
  <alternateIdentifiers>
    <alternateIdentifier alternateIdentifierType="url">https://aperta.ulakbim.gov.tr/record/29971</alternateIdentifier>
  </alternateIdentifiers>
  <relatedIdentifiers>
    <relatedIdentifier relatedIdentifierType="DOI" relationType="IsIdenticalTo">10.3389/fped.2018.00200</relatedIdentifier>
  </relatedIdentifiers>
  <rightsList>
    <rights rightsURI="http://www.opendefinition.org/licenses/cc-by">Creative Commons Attribution</rights>
    <rights rightsURI="info:eu-repo/semantics/openAccess">Open Access</rights>
  </rightsList>
  <descriptions>
    <description descriptionType="Abstract">Background: Steroid resistant nephrotic syndrome (SRNS) is a rare condition, accounting for 10-15% of all children with idiopathic nephrotic syndrome. SRNS can be caused by genetic abnormalities or immune system dysfunction. The prognosis of SRNS varies from permanent remission to progression to end-stage kidney disease, and post-transplant recurrence is common.</description>
  </descriptions>
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