Yayınlanmış 1 Ocak 2018 | Sürüm v1
Dergi makalesi Açık

Type I IFN-related NETosis in ataxia telangiectasia and Artemis deficiency

  • 1. Middle East Tech Univ, Dept Biol Sci, TR-06800 Ankara, Turkey
  • 2. Necmettin Erbakan Univ, Meram Med Fac, Dept Immunol & Allergy, Konya, Turkey
  • 3. Ihsan Dogramaci Bilkent Univ, Dept Mol Biol & Genet, Therapeut Oligodeoxynucleotide Res Lab, Thorlab, Ankara, Turkey
  • 4. Necmettin Erbakan Univ, Meram Med Fac, Dept Pathol, Konya, Turkey
  • 5. Acibadem Mehmet Ali Aydinlar Univ, Dept Mol Biol & Genet, Istanbul, Turkey
  • 6. Hacettepe Univ, Fac Med, Dept Radiol, Ankara, Turkey
  • 7. Hacettepe Univ, Fac Med, Dept Pediat Immunol, Ankara, Turkey
  • 8. Hacettepe Univ, Fac Med, Dept Pediat Rheumatol, Ankara, Turkey

Açıklama

Background: Pathological inflammatory syndromes of unknown etiology are commonly observed in ataxia telangiectasia (AT) and Artemis deficiency. Similar inflammatory manifestations also exist in patients with STING-associated vasculopathy in infancy (SAVI).

Dosyalar

bib-c54e35e0-fdc0-44ba-ae74-1d7374a262b7.txt

Dosyalar (387 Bytes)

Ad Boyut Hepisini indir
md5:c1448104bde9df1f27b2c8b68cfc66f4
387 Bytes Ön İzleme İndir