Yayınlanmış 1 Ocak 2021 | Sürüm v1
Dergi makalesi Açık

Identification of novel TUBB1 variants in patients with macrothrombocytopenia

  • 1. Gebze Tech Univ, Dept Mol Biol & Genet, Fac Sci, Kocaeli, Turkey
  • 2. Dr Behcet Uz Childrens Hosp, Dept Pediat Hematol, Izmir, Turkey
  • 3. TOBB ETU Univ, Dept Pediat, Fac Med, Ankara, Turkey
  • 4. Istanbul Okan Univ, Vocat Sch Hlth Serv, Med Lab, Istanbul, Turkey

Açıklama

Background/aim: Macrothrombocytopenia is an autosomal-dominant disorder characterized by increased platelet size and a decreased number of circulating platelets. The membrane skeleton and the link between actin filaments of the skeleton and microtubules, which consist of alpha and beta tubulin [including the tubulin beta-1 chain (TUBB1)] heterodimers, are important for normal platelet morphology, and defects in these systems are associated with macrothrombocytopenia.

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